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KMID : 0882420060700000328
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Korean Journal of Medicine
2006 Volume.70 No. 0 p.328 ~ p.334
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A case of POEMS syndrome in a 15-year-old boy
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Lee Dan-Bi
Bae Jung-Ho
Yeo Young-Sun
Lee Chang-Keun
Kim Shin
Shon Hee-Jeong
Suh Chul-Won
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Abstract
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POEMS syndrome is a rare multisystemic disorder characterized by polyneuropathy, organomegaly, endocrinopathy, monoclonal gammopathy, and skin change. Although patients with POEMS are usually younger than symptomatic multiple myeloma patients, the median age of patients with POEMS syndrome is reported to be 51 years (range: 30 to 83 years). A 15-year-old boy visited our hospital because of progressive lower extremity weakness and gait disturbance. He showed
polyneuropathy, hepatosplenomegaly, hypogonadism, hyperprolactinemia, adrenal insufficiency, IgG lambda type monoclonal gammopathy, hyperpigmentation, hypertrichosis, and skin thickening, which we diagnosed as POEMS syndrome. This might be the youngest case of POEMS syndrome in Korea; thus we report here with a review of literatures.(Korean J Med 70:S328-S334, 2006)
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KEYWORD
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POEMS syndrome, Age, Autologous stem cell transplantation
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